Diamond Blackfan Anemia
《英文msh詞典》Diamond Blackfan Anemia
[入口詞] Diamond Blackfan Anemia
[主題詞] Anemia,Diamond-Blackfan
[英文釋義] A rare congenital hypoplastic anemia that usually presents early in infancy. The disease is characterized by a moderate to severe macrocytic anemia,occasional neutropenia or thrombocytosis,a normocellular bone marrow with erythroid hypoplasia,and an increased risk of developing leukemia. (Curr Opin Hematol 2000 Mar;7(2):85-94)